Case Report


Darier and Ferrand dermatofibrosarcoma: A case report of an unusual presentation and literature review

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1 Department of Digestive Oncology Surgery, Mohammed V University of Rabat, Ibn Sina University Hospital Centre, National Institute of Oncology, Rabat, Morocco

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Prosper Nsengiyumva

Department of Digestive Oncology Surgery, Mohamed V University of Rabat, Ibn Sina University Hospital Centre, National Institute of Oncology, Rabat,

Morocco

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Article ID: 100121Z12PN2023

doi: 10.5348/100121Z12PN2023CR

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How to cite this article

Nsengiyumva P, Kabbaj T, Majbar MA, Benkabbou A, Souadka A, Mohsine R. Darier and Ferrand dermatofibrosarcoma: A case report of an unusual presentation and literature review. J Case Rep Images Surg 2023;9(2):1–6.

ABSTRACT


Dermatofibrosarcoma is a rare fibrous tumor of the skin. Its evolution is slow and indolent with a high potential for recurrence. We report a case of Darier and Ferrand dermatofibrosarcoma that had progressed in a 56-year-old female patient from childhood. Clinical examination revealed an indurated, round, budding, ulcerative mass located to the left hypochondrium. This mass was painful, hard, and mobile at deep levels. Computed tomography of the thorax, abdomen, and pelvis showed no lesions other than a mass in the left hypochondrium. Immunohistochemical studies of previously performed biopsies were unremarkable. A histologic examination of the surgical specimen confirmed the diagnosis. The further course after 12 months was uneventful.

Keywords: Dermatofibrosarcoma, Difficulties in diagnosis and treatment, Slow and indolent course

SUPPORTING INFORMATION


Author Contributions

Prosper Nsengiyumva - Substantial contributions to conception and design, Drafting the article, Final approval of the version to be published

Taha Kabbaj - Acquisition of data, Drafting the article, Final approval of the version to be published

Mohamed Anass Majbar - Substantial contributions to conception and design, Interpretation of data, Revising it critically for important intellectual content, Final approval of the version to be published

Amine Benkabbou - Analysis of data, Revising it critically for important intellectual content, Final approval of the version to be published

Amine Souadka - Interpretation of data, Revising it critically for important intellectual content, Final approval of the version to be published

Raouf Mohsine - Interpretation of data, Revising it critically for important intellectual content, Final approval of the version to be published

Acknowledgments

Thanks go to all authors for completing this noble work.

Guarantor of Submission

The corresponding author is the guarantor of submission.

Source of Support

None

Consent Statement

Written informed consent was obtained from the patient for publication of this article.

Data Availability

All relevant data are within the paper and its Supporting Information files.

Conflict of Interest

Authors declare no conflict of interest.

Copyright

© 2023 Prosper Nsengiyumva et al. This article is distributed under the terms of Creative Commons Attribution License which permits unrestricted use, distribution and reproduction in any medium provided the original author(s) and original publisher are properly credited. Please see the copyright policy on the journal website for more information.